Indian Journal of Dermatology
CASE REPORT
Year
: 2009  |  Volume : 54  |  Issue : 2  |  Page : 168--172

Clear cell sarcoma: A case mimicking primary cutaneous malignant melanoma


M Rodriguez-Martin1, M Saez-Rodriguez1, B Esquivel2, R Sanchez Gonzalez1, A Noda Cabrera1, A Martin Herrera2 
1 Department of Dermatology, Hospital Universitario de Canarias, University of La Laguna, 38320 - La Laguna, Tenerife, Spain
2 Department of Pathology, Hospital Universitario de Canarias, University of La Laguna, 38320 - La Laguna, Tenerife, Spain

Correspondence Address:
M Rodriguez-Martin
Dermatology Department, Hospital Universitario de Canarias, Ofra s/n. La Laguna, Santa Cruz de Tenerife, 38320 Canary Islands
Spain

Clear cell sarcoma (CCS) is a recently described variant of sarcoma characterized by prominent clear cells showing features similar to clear cell melanoma. This neoplasm was first described by Dr. Franz M. Erzinger. Primary CCS usually arises in deeper soft tissues, in association with fascia, tendons, or aponeuroses. Characteristic translocation t(12;22) (q13;q12) has been considered pathognomonic for CCS. Prognosis is related to tumor size. An early recognition and initial radical surgery is the key to a favourable outcome. We present a patient with an unusual neoplasm that resembled malignant melanoma.


How to cite this article:
Rodriguez-Martin M, Saez-Rodriguez M, Esquivel B, Gonzalez R S, Cabrera A N, Herrera A M. Clear cell sarcoma: A case mimicking primary cutaneous malignant melanoma.Indian J Dermatol 2009;54:168-172


How to cite this URL:
Rodriguez-Martin M, Saez-Rodriguez M, Esquivel B, Gonzalez R S, Cabrera A N, Herrera A M. Clear cell sarcoma: A case mimicking primary cutaneous malignant melanoma. Indian J Dermatol [serial online] 2009 [cited 2013 May 22 ];54:168-172
Available from: http://www.e-ijd.org/article.asp?issn=0019-5154;year=2009;volume=54;issue=2;spage=168;epage=172;aulast=Rodriguez-Martin;type=0