Source of Support: None, Conflict of Interest: None
A 8 year old girl developed palmoplanter keratoderma at the age of three years. At the same time she developed star shaped keratotic plaques on dorsa of hands, feet and knees. After eight months, pseudoainhum developed which deepened later on leading to autompution. She was deal and dumb since birth. A typical case of keratoderma mutilans of vohwinkel is described for its rarity.